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DeCS
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Descriptor English:
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Histiocytosis, Langerhans-Cell
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Descriptor Spanish:
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Histiocitosis de Células de Langerhans
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Descriptor Portuguese:
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Histiocitose de Células de Langerhans
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Synonyms English:
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Histiocytosis X
Langerhans-Cell Granulomatosis
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Tree Number:
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C08.381.483.375
C15.604.667.400.400
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Definition English:
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Group of disorders characterized by monoclonal proliferation of CD1+ HISTIOCYTES. The demonstration of the LANGERHANS CELLS Birbeck granules is the gold standard of the phenotype. EOSINOPHILIC GRANULOMA makes up 60-80% of all the cases. |
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Indexing Annotation English:
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GEN or unspecified; prefer specifics
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History Note English:
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90(75); was see under RETICULOENDOTHELIOSIS 1966-75; was HISTIOCYTOSIS X 1975-89
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Allowable Qualifiers English:
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Record Number:
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28223
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Unique Identifier:
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D006646
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Occurrence in VHL:
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Similar:
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DeCS SciELO LILACS LIS
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